Katharine Hunter Cook

Aggressive Systemic Mastocytosis Resulting in Hepatic Fibrosis and Non-Cirrhotic Portal Hypertension

Aggressive systemic mastocytosis [ASM] is a rare hematologic disorder characterized by mast cell infiltration of extracutaneous organs. Hepatic involvement is uncommon and rarely progresses to fibrosis or portal hypertension. We present a 60-year-old male with abdominal distensio...