Bruno Crestani

Bronchial artery hypertrophy: a novel vascular manifestation of telomere biology disorders in pulmonary fibrosis

Fibrosing interstitial lung diseases (ILD) associated with telomere-related gene (TRG) mutations exhibit extra-thoracic features suggesting systemic angiogenesis abnormalities. We investigated the bronchial arterial circulation in TRG-mutated ILD patients. We measured right and l...